Vascular reactivity and pulmonary hypertension in systemic sclerosis
نویسندگان
چکیده
منابع مشابه
Pulmonary hypertension in systemic sclerosis.
A woman born in 1912 (Case 8 in the necropsy series) had an unremarkable family history. In 1940, she first noted blanching and cyanosis of the fingers on exposure to cold. Since 1960, small, hard, subcutaneous nodules developed at different locations on her body. Early in 1968, progressive effort dypsnoea and anginal chest pains started insidiously, and treatment with digitalis, furosemide, an...
متن کاملPulmonary hypertension in systemic sclerosis: different phenotypes.
Pulmonary hypertension (PH) is a frequent and severe complication of systemic sclerosis (SSc). PH in SSc is highly heterogeneous because of the various clinical phenotypes of SSc itself and because the mechanisms of PH can vary from one patient to another. PH in SSc may be due to vasculopathy of the small pulmonary arteries (group 1; pulmonary arterial hypertension), interstitial lung disease (...
متن کاملPulmonary arterial hypertension in systemic sclerosis.
Pulmonary arterial hypertension (PAH) in systemic sclerosis (SSc) is a complex clinical situation resulting from restricted flow through the pulmonary arterial circulation ending in increased pulmonary vascular resistance and right heart failure. PAH is a common and life-threatening complication in connective tissue diseases, specifically in SSc if not treated rapidly and adequately. Based on t...
متن کاملPrevalence of pulmonary hypertension in systemic sclerosis.
OBJECTIVE To assess the prevalence of pulmonary arterial hypertension (PAH) in patients with the diagnosis of systemic sclerosis (SSc) followed at a tertiary university service. MATERIAL AND METHODS Fifty-seven patients with SSc were studied by clinical assessment directed at the cardiopulmonary system, pulmonary function tests and Doppler echocardiography (ECHO). The following criteria were ...
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Pulmonary arterial hypertension (PAH) is a severe manifestation of systemic sclerosis (SSc) and systemic lupus erythematosus (SLE). Due to improvements in the understanding of the pathogenesis of these diseases, improved methodological rigour in the conduct of epidemiological studies and the advent of successful therapies, our understanding of SSc-PAH and SLE-PAH has evolved considerably. In th...
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ژورنال
عنوان ژورنال: Arthritis & Rheumatism
سال: 1983
ISSN: 0004-3591,1529-0131
DOI: 10.1002/art.1780260815